ABSTRACT
Interstitial lung diseases (ILD), are associated with a high incidence of pulmonary hypertension (PH), which is linked with exercise limitation and a worse prognosis. Apart from Idiopathic pulmonary fibrosis, PH can occur in connective tissue diseases and sarcoidosis. Echocardiography and right heart catheterization are crucial modalities for the diagnosis of PH. Rare lung diseases are important pathologies that may create interstitial patterns in the lungs and should always be known and considered in the differential diagnosis of ILD.
Keywords: Pulmonary hypertension, interstitial lung disease, lung fibrosis
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